闭塞性细支气管炎伴机化性肺炎( idiopathic bronchiolitis obliterans organizing pneumonia , BOOP )是一种弥漫性的ILD ,分为特发性和继发性。继发性BOOP一般见于结缔组织病肺损伤、药物反应和某些感染之后,如果原因不明则称之为特发性BOOP ,与隐源性机化性肺炎( cryptogenic organizing pneumonia , COP )为同一概念,是特发性间质性肺炎( idiopathic interstitial pneumonia ......